gastroesophageal le iomyomatosis in a young woman with v ulvar leiomyomatosis and gallstone disease: report of a rare case

gastroesophageal-vul var leiomyomatosis is a very rare condition it is characterized by diffuse, ill-defined proliferation of smooth muscle in the esophagus and vulva. we present an interesting case of esophageal leiomyomatosis in a woman with a history of vulvar leiomyomatosis and a gall bladder full of stones. she was 18-years old and had a 4 year history of vulvar mass and clitoromegaly, with subclinical dysphagia. this paper represents the first reported simultaneous occurrence of these three pathologic entities in the english literature. esophago-vulvar leiomyomatosis should be considered in a young patient with vulvar mass and long-standing dysphagia in whom a smooth, tapered esophageal narrowing on barium study and circumferential esophageal wall thickening on ct scan are seen. an esophagectomy combined with a reconstruction procedure is indicated.